DENTINOGENESIS IMPERFECTA TYPE I: CASE REPORT AND MICROSCOPIC ANALYSIS OF DENTINAL TISSUE

Abstract

Introdution: Dentinogenesis Imperfecta (DI) affects the dentin of deciduous and permanent teeth. It may be associated with a hereditary and systemic bone disorder known as Osteogenesis Imperfecta.  Case Report: to report the case of an 11- year-old patient diagnosed with DI type I, who had two deciduous molars affected by the disease extracted. The extracted teeth underwent histological analysis and evaluation using Confocal Laser Microscopy, Histologically, disorganized tubules with different diameters and in lesser quantity were observed, and collagen fibrils exhibited irregular distribution. Results: Confocal microscopy showed dysplastic dentin, irregular tubules, areas devoid of dentinal tubules, and granule deposition. Conclusions: Dentinogenesis imperfecta (DI) compromises  the formation of dentinal tubules, which may affect the structural and mechanical properties of dentin. Furthermore, it can lead to tooth fractures and wear, thereby impacting oral health and aesthetics.